E88.4
Header — not billableMitochondrial metabolism disorders
The ICD-10 code for mitochondrial metabolism disorders is E88.4.
E88.4 is a non-billable header code. It groups related conditions but cannot be used on its own for reimbursement — select one of the 5 more specific codes below.
Clinical notes
Excludes1 (not coded here)
An Excludes1 note is a pure exclusion: the excluded condition and this code should never be reported together, because the two conditions cannot occur at the same time (e.g. a congenital form vs. an acquired form of the same disease).
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •This is a non-billable header code. Documentation must support a more specific child code before this diagnosis can be reported on a claim.
- •Confirm the excluded condition(s) listed above are not also present — Excludes1 conditions cannot be coded together with this one.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- E88.0Disorders of plasma-protein metabolism, not elsewhere classifiednon-billable header
- E88.1Lipodystrophy, not elsewhere classifiednon-billable header
- E88.2Lipomatosis, not elsewhere classified
- E88.3Tumor lysis syndrome
- E88.8Other specified metabolic disordersnon-billable header
- E88.9Metabolic disorder, unspecified
- E88.AWasting disease (syndrome) due to underlying condition
- E88.4Mitochondrial metabolism disordersnon-billable header