E88.40
Billable codeMitochondrial metabolism disorder, unspecified
The ICD-10 code for mitochondrial metabolism disorder, unspecified is E88.40.
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •This code describes an unspecified presentation. If the medical record documents a more specific detail (e.g. laterality, type, or affected site), a more specific sibling code should be used instead — see Related codes below.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- E88.41MELAS syndrome
- E88.42MERRF syndrome
- E88.43Disorders of mitochondrial tRNA synthetases
- E88.49Other mitochondrial metabolism disorders
- E88.40Mitochondrial metabolism disorder, unspecified
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 27787Approximate match
Associated MS-DRGs
E88.40 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.