E88.43
Billable codeDisorders of mitochondrial tRNA synthetases
The ICD-10 code for disorders of mitochondrial trna synthetases is E88.43.
Clinical notes
Code also
Two codes may be needed to fully describe a condition, but unlike Code First/Use Additional Code, the sequencing order is not mandated by convention.
- , if applicable, associated condition such as:
- leukoencephalopathy (G93.49)
Also known as
Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.
- ARS2-related mitochondrial disorders
- LBSL
- Leukoencephalopathy with brainstem - spinal cord involvement - lactate elevation
- Leukoencephalopathy with thalamus - brainstem involvement - high lactate
- LTBL
- Mitochondrial aminoacyl-tRNA synthetase disorders
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- E88.40Mitochondrial metabolism disorder, unspecified
- E88.41MELAS syndrome
- E88.42MERRF syndrome
- E88.49Other mitochondrial metabolism disorders
- E88.43Disorders of mitochondrial tRNA synthetases
Associated MS-DRGs
E88.43 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.