10ICD Code Hub

H49.81

Header — not billable

Kearns-Sayre syndrome

The ICD-10 code for kearns-sayre syndrome is H49.81.

H49.81 is a non-billable header code. It groups related conditions but cannot be used on its own for reimbursement — select one of the 4 more specific codes below.

Clinical notes

Code also

Two codes may be needed to fully describe a condition, but unlike Code First/Use Additional Code, the sequencing order is not mandated by convention.

  • , if applicable, other manifestations, such as:
  • heart block (I45.9)

Also known as

Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.

  • Progressive external ophthalmoplegia with pigmentary retinopathy

Documentation support

General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.

Child codes under H49.81

Related codes in this category