N01.A

Billable code

Rapidly progressive nephritic syndrome with C3 glomerulonephritis

The ICD-10 code for rapidly progressive nephritic syndrome with c3 glomerulonephritis is N01.A.

Clinical notes

Excludes1 (not coded here)

An Excludes1 note is a pure exclusion: the excluded condition and this code should never be reported together, because the two conditions cannot occur at the same time (e.g. a congenital form vs. an acquired form of the same disease).

Rapidly progressive nephritic syndrome (with C3 glomerulopathy) with dense deposit disease (N01.6)

Also known as

Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.

Rapidly progressive nephritic syndrome with C3 glomerulopathy, NOS

Documentation support

General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.

•Confirm the excluded condition(s) listed above are not also present — Excludes1 conditions cannot be coded together with this one.
•As a general rule, code to the highest level of specificity supported by the documentation in the medical record.

Related codes in this category

Associated MS-DRGs

N01.A can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.

Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.