N01
Header — not billableRapidly progressive nephritic syndrome
The ICD-10 code for rapidly progressive nephritic syndrome is N01.
N01 is a non-billable header code. It groups related conditions but cannot be used on its own for reimbursement — select one of the 11 more specific codes below.
Clinical notes
Excludes1 (not coded here)
An Excludes1 note is a pure exclusion: the excluded condition and this code should never be reported together, because the two conditions cannot occur at the same time (e.g. a congenital form vs. an acquired form of the same disease).
- nephritic syndrome NOS (N05.-)
Includes
Terms listed here further define or give examples of the conditions grouped under this code — they describe what the code covers, not a separate diagnosis.
- rapidly progressive glomerular disease
- rapidly progressive glomerulonephritis
- rapidly progressive nephritis
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •This is a non-billable header code. Documentation must support a more specific child code before this diagnosis can be reported on a claim.
- •Confirm the excluded condition(s) listed above are not also present — Excludes1 conditions cannot be coded together with this one.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Child codes under N01
- N01.0Rapidly progressive nephritic syndrome with minor glomerular abnormality
- N01.1Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
- N01.2Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
- N01.3Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
- N01.4Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
- N01.5Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
- N01.6Rapidly progressive nephritic syndrome with dense deposit disease
- N01.7Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
- N01.8Rapidly progressive nephritic syndrome with other morphologic changes
- N01.9Rapidly progressive nephritic syndrome with unspecified morphologic changes
- N01.ARapidly progressive nephritic syndrome with C3 glomerulonephritis
Related codes in this category
- N00Acute nephritic syndromenon-billable header
- N02Recurrent and persistent hematurianon-billable header
- N03Chronic nephritic syndromenon-billable header
- N04Nephrotic syndromenon-billable header
- N05Unspecified nephritic syndromenon-billable header
- N06Isolated proteinuria with specified morphological lesionnon-billable header
- N07Hereditary nephropathy, not elsewhere classifiednon-billable header
- N08Glomerular disorders in diseases classified elsewhere
- N01Rapidly progressive nephritic syndromenon-billable header