D81.818
Billable codeOther biotin-dependent carboxylase deficiency
The ICD-10 code for other biotin-dependent carboxylase deficiency is D81.818.
Clinical notes
Also known as
Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.
- Holocarboxylase synthetase deficiency
- Other multiple carboxylase deficiency
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- D81.810Biotinidase deficiency
- D81.819Biotin-dependent carboxylase deficiency, unspecified
- D81.818Other biotin-dependent carboxylase deficiency
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 2662Approximate match
Associated MS-DRGs
D81.818 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.