Q98.1
Billable codeKlinefelter syndrome, male with more than two X chromosomes
The ICD-10 code for klinefelter syndrome, male with more than two x chromosomes is Q98.1.
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- Q98.0Klinefelter syndrome karyotype 47, XXY
- Q98.3Other male with 46, XX karyotype
- Q98.4Klinefelter syndrome, unspecified
- Q98.5Karyotype 47, XYY
- Q98.6Male with structurally abnormal sex chromosome
- Q98.7Male with sex chromosome mosaicism
- Q98.8Other specified sex chromosome abnormalities, male phenotype
- Q98.9Sex chromosome abnormality, male phenotype, unspecified
- Q98.1Klinefelter syndrome, male with more than two X chromosomes
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 7587Approximate match
Associated MS-DRGs
Q98.1 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.