Q26.2
Billable codeTotal anomalous pulmonary venous connection
The ICD-10 code for total anomalous pulmonary venous connection is Q26.2.
Clinical notes
Also known as
Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.
- Total anomalous pulmonary venous return [TAPVR], subdiaphragmatic
- Total anomalous pulmonary venous return [TAPVR], supradiaphragmatic
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •Laterality-specific codes exist for this condition — confirm the affected side is documented.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- Q26.0Congenital stenosis of vena cava
- Q26.1Persistent left superior vena cava
- Q26.3Partial anomalous pulmonary venous connection
- Q26.4Anomalous pulmonary venous connection, unspecified
- Q26.5Anomalous portal venous connection
- Q26.6Portal vein-hepatic artery fistula
- Q26.8Other congenital malformations of great veins
- Q26.9Congenital malformation of great vein, unspecified
- Q26.2Total anomalous pulmonary venous connection
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 74741
Associated MS-DRGs
Q26.2 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.