K00.4
Billable codeDisturbances in tooth formation
The ICD-10 code for disturbances in tooth formation is K00.4.
Clinical notes
Excludes1 (not coded here)
An Excludes1 note is a pure exclusion: the excluded condition and this code should never be reported together, because the two conditions cannot occur at the same time (e.g. a congenital form vs. an acquired form of the same disease).
- Hutchinson's teeth and mulberry molars in congenital syphilis (A50.5)
Excludes2 (not included here)
An Excludes2 note means the excluded condition is not part of this one, but a patient can have both at the same time — in that case both codes may be reported together.
- mottled teeth (K00.3)
Also known as
Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.
- Aplasia and hypoplasia of cementum
- Dilaceration of tooth
- Enamel hypoplasia (neonatal) (postnatal) (prenatal)
- Regional odontodysplasia
- Turner's tooth
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •Confirm the excluded condition(s) listed above are not also present — Excludes1 conditions cannot be coded together with this one.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- K00.0Anodontia
- K00.1Supernumerary teeth
- K00.2Abnormalities of size and form of teeth
- K00.3Mottled teeth
- K00.5Hereditary disturbances in tooth structure, not elsewhere classified
- K00.6Disturbances in tooth eruption
- K00.7Teething syndrome
- K00.8Other disorders of tooth development
- K00.9Disorder of tooth development, unspecified
- K00.4Disturbances in tooth formation
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 5204
Associated MS-DRGs
K00.4 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.
- DRG 011Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy with MCC
- DRG 012Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy with CC
- DRG 013Tracheostomy for Face, Mouth and Neck Diagnoses or Laryngectomy without CC/MCC
- DRG 157Dental and Oral Diseases with MCC
- DRG 158Dental and Oral Diseases with CC
- DRG 159Dental and Oral Diseases without CC/MCC