10ICD Code Hub

I27.841

Billable code

Fontan-associated lymphatic dysfunction

The ICD-10 code for fontan-associated lymphatic dysfunction is I27.841.

Clinical notes

Code also

Two codes may be needed to fully describe a condition, but unlike Code First/Use Additional Code, the sequencing order is not mandated by convention.

  • associated conditions such as:
  • chylothorax (J94.0)
  • Fontan associated protein-losing enteropathy (K90.89)
  • plastic (obstructive) bronchitis (J44.89)

Documentation support

General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.

Related codes in this category

Associated MS-DRGs

I27.841 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.

Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.