E83.822
Billable codeENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2
The ICD-10 code for enpp1 deficiency causing autosomal recessive hypophosphatemic rickets type 2 is E83.822.
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- E83.820Generalized arterial calcification of infancy with unspecified genetic causality
- E83.821ENPP1 deficiency causing generalized arterial calcification of infancy
- E83.823ABCC6 deficiency causing generalized arterial calcification of infancy
- E83.824ABCC6 deficiency causing pseudoxanthoma elasticum
- E83.825CD73 deficiency causing arterial calcification
- E83.822ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2
Associated MS-DRGs
E83.822 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.