E80.0
Billable codeHereditary erythropoietic porphyria
The ICD-10 code for hereditary erythropoietic porphyria is E80.0.
Clinical notes
Also known as
Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.
- Congenital erythropoietic porphyria
- Erythropoietic protoporphyria
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- E80.1Porphyria cutanea tarda
- E80.2Other and unspecified porphyrianon-billable header
- E80.3Defects of catalase and peroxidase
- E80.4Gilbert syndrome
- E80.5Crigler-Najjar syndrome
- E80.6Other disorders of bilirubin metabolism
- E80.7Disorder of bilirubin metabolism, unspecified
- E80.0Hereditary erythropoietic porphyria
ICD-9-CM equivalent
Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.
- 2771Approximate match
Associated MS-DRGs
E80.0 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.