E78.010
Billable codeHomozygous familial hypercholesterolemia [HoFH]
The ICD-10 code for homozygous familial hypercholesterolemia [hofh] is E78.010.
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
- E78.011Heterozygous familial hypercholesterolemia [HeFH]
- E78.019Familial hypercholesterolemia, unspecified
- E78.010Homozygous familial hypercholesterolemia [HoFH]
Associated MS-DRGs
E78.010 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.