E75.244
Billable codeNiemann-Pick disease type A/B
The ICD-10 code for niemann-pick disease type a/b is E75.244.
Clinical notes
Also known as
Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.
- Acid sphingomyelinase deficiency type A/B (ASMD type A/B)
- Chronic neurovisceral acid sphingomyelinase deficiency
Documentation support
General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.
- •As a general rule, code to the highest level of specificity supported by the documentation in the medical record.
Related codes in this category
Associated MS-DRGs
E75.244 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.
Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.