10ICD Code Hub

E72.4

Billable code

Disorders of ornithine metabolism

The ICD-10 code for disorders of ornithine metabolism is E72.4.

Clinical notes

Excludes1 (not coded here)

An Excludes1 note is a pure exclusion: the excluded condition and this code should never be reported together, because the two conditions cannot occur at the same time (e.g. a congenital form vs. an acquired form of the same disease).

  • hereditary choroidal dystrophy (H31.2-)

Also known as

Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.

  • Hyperammonemia-Hyperornithinemia-Homocitrullinemia syndrome
  • Ornithinemia (types I, II)
  • Ornithine transcarbamylase deficiency

Documentation support

General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.

Related codes in this category

ICD-9-CM equivalent

Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.

View full ICD-10 → ICD-9 crosswalk →

Associated MS-DRGs

E72.4 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.

Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.