10ICD Code Hub

D47.02

Billable code

Systemic mastocytosis

The ICD-10 code for systemic mastocytosis is D47.02.

Clinical notes

Code also

Two codes may be needed to fully describe a condition, but unlike Code First/Use Additional Code, the sequencing order is not mandated by convention.

  • , if applicable, any associated hematological non-mast cell lineage disease, such as:
  • acute myeloid leukemia (C92.6-, C92.A-)
  • chronic myelomonocytic leukemia (C93.1-)
  • essential thrombocytosis (D47.3)
  • hypereosinophilic syndrome (D72.1)
  • myelodysplastic syndrome (D46.9)
  • myeloproliferative syndrome (D47.1)
  • non-Hodgkin lymphoma (C82-C85)
  • plasma cell myeloma (C90.0-)
  • polycythemia vera (D45)

Excludes1 (not coded here)

An Excludes1 note is a pure exclusion: the excluded condition and this code should never be reported together, because the two conditions cannot occur at the same time (e.g. a congenital form vs. an acquired form of the same disease).

  • aggressive systemic mastocytosis (C96.21)
  • mast cell leukemia (C94.3-)

Also known as

Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.

  • Indolent systemic mastocytosis
  • Isolated bone marrow mastocytosis
  • Smoldering systemic mastocytosis
  • Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)

Documentation support

General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.

Related codes in this category

ICD-9-CM equivalent

Informational only — GEM mappings are approximate, not guaranteed one-to-one equivalents. Verify before use in billing.

View full ICD-10 → ICD-9 crosswalk →

Associated MS-DRGs

D47.02 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.

Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.