C83.390: Primary central nervous system lymphoma

Clinical notes

Excludes1 (not coded here)

An Excludes1 note is a pure exclusion: the excluded condition and this code should never be reported together, because the two conditions cannot occur at the same time (e.g. a congenital form vs. an acquired form of the same disease).

Primary central nervous system lymphoma, Burkitt (C83.79)
Primary central nervous system lymphoma, lymphoblastic (C83.59)
Primary central nervous system lymphoma, other (C83.89)
Primary central nervous system lymphoma, peripheral T-cell (C84.49)

Also known as

Alternate wording, synonyms, or specific conditions that fall under this code, listed to help confirm you've picked the right one.

PCNSL of brain
PCNSL of meninges
PCNSL of spinal cord
PCNSL NOS

Documentation support

General coding-documentation guidance — not a substitute for payer-specific requirements or professional coding judgment.

•Confirm the excluded condition(s) listed above are not also present — Excludes1 conditions cannot be coded together with this one.
•As a general rule, code to the highest level of specificity supported by the documentation in the medical record.

Related codes in this category

C83.398Diffuse large B-cell lymphoma of other extranodal and solid organ sites
C83.390Primary central nervous system lymphoma

Associated MS-DRGs

C83.390 can serve as the principal diagnosis for these Medicare Severity Diagnosis-Related Groups.

Informational only — actual DRG assignment also depends on procedures, complications/comorbidities (CC/MCC), discharge status, and payer-specific rules not reflected here.